Cardiac function in muscular dystrophy associates with abdominal muscle pathology
نویسندگان
چکیده
منابع مشابه
Cardiac function in muscular dystrophy associates with abdominal muscle pathology.
BACKGROUND The muscular dystrophies target muscle groups differentially. In mouse models of muscular dystrophy, notably the mdx model of Duchenne Muscular Dystrophy, the diaphragm muscle shows marked fibrosis and at an earlier age than other muscle groups, more reflective of the histopathology seen in human muscular dystrophy. METHODS Using a mouse model of limb girdle muscular dystrophy, the...
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ژورنال
عنوان ژورنال: Journal of Neuromuscular Diseases
سال: 2015
ISSN: 2214-3599
DOI: 10.3233/jnd-140062